| 克隆類型 ： |
Rabbit Polyclonal Antibody, HRP-conjugated Antibody |
|
亞 型 ： |
Rabbit Ig |
|
免 疫 原 ： |
KLH-conjugated synthetic peptide encompassing a sequence within the N-term region of mouse AMACR. |
|
產(chǎn)品描述 ： |
Alpha-methylacyl-CoA racemase (AMACR) catalyzes the racemization of 2-methyl-branched fatty acid CoA esters. AMACR is responsible for the conversion of pristanoyl-CoA and C27-bile acyl-CoAs to their (S)-stereoisomers. Defects in AMACR are the cause of alpha-methylacyl-CoA racemase deficiency (AMACRD). AMACRD results in elevated plasma concentrations of pristanic acid C27-bile-acid intermediates. AMACRD is associated with polyneuropathy, retinitis pigmentosa, epilepsy. |
| 適用物種 ： |
H, M, R |
|
應(yīng)用范圍 ： |
E, WB, IHC |
| 應(yīng)用說明 ： |
E: 1:500-1:1,000; WB: 1:200-1:500; IHC: 1:50-1:500 |
| 別 名 ： |
AMACR; Alpha-methylacyl-CoA racemase; 2-methylacyl-CoA racemase |
|
形 態(tài) ： |
Each vial contains 0.1 mg IgG in 0.1 ml (1 mg/ml) of PBS pH7.4, 1% BSA and 0.02% gentamicin. Antibody was purified by Protein-G affinity chromatography. |
| 保存條件 ： |
Store at -20°C. Product is guaranteed 6 months from the date of shipment. |
| 產(chǎn)品鏈接 ： |
http://www.abbiotec.com/antibodies/amacr-antibody-0 |
| 標(biāo) 記 物 ： |
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產(chǎn)品說明 ： |
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