| 克隆類型 ： |
Mouse Monoclonal Antibody |
|
亞 型 ： |
Mouse IgG1 |
|
免 疫 原 ： |
Chicken breast nebulin. |
|
產(chǎn)品描述 ： |
Nebulin is a large muscle protein involved in maintaining the structural integrity of sarcomeres and the membrane system associated with the myofibrils. Nebulin binds and stabilizes F-actin. Defects in nebulin are the cause of nemaline myopathy type 2 (NEM2). NEM2 is a form of nemaline myopathy. Nemaline myopathies are muscular disorders characterized by muscle weakness of varying severity and onset, and abnormal thread or rod-like structures in muscle fibers on histologic examination. |
| 適用物種 ： |
H, M, R, Ck, X |
|
應用范圍 ： |
E, WB |
| 應用說明 ： |
E: 1:500-1:1,000; WB: 1:100-1:500 |
| 別 名 ： |
Nebulin; NEB |
|
形 態(tài) ： |
Each vial contains 0.1 mg IgG in 0.1 ml (1 mg/ml) of PBS pH7.4, 2% BSA with 0.09% sodium azide. Antibody was purified by Protein-G affinity chromatography. |
| 保存條件 ： |
Store at -20°C. Minimize freeze-thaw cycles. Product is guaranteed one year from the date of shipment. |
| 產(chǎn)品鏈接 ： |
http://www.abbiotec.com/antibodies/nebulin-antibody |
| 標 記 物 ： |
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產(chǎn)品說明 ： |
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